Case Report on: Dandy Walker Malformation Syndrome

Khushbu Meshram,Pooja Kasturkar,Prerana Sakharwade,Shital Sakharkar,Sonali Kolhekar

doi:10.9734/jpri/2021/v33i44b32660

Abstract

Introduction: Dandy Walker Syndrome is a congenital brain malformation that affects the cerebellum and the fluid filled areas that accompany it. The cerebellum is a part of the brain that deals with movement coordination as well as cognition and behavior. Case Presentation: The male patient 8 year old who was apparently admitted in A.V.B.R.H on 18/8/2019 is diagnosed with a known case of dandy walker malformation and came with the complaints of headache since 4 days, fever since 3 days, vomiting since 5 days and 3 episodes of seizures. All the necessary blood investigations has been done. The CT scan as well as MRI reports has shown that large posterior fossa cyst with open communication with fourth ventricle with hypoplastic left cerebellar hemisphere and no visualized cerebellar vermis. Before taking this case, information was given to the patients and their relatives and Informed consent was obtained from patient as well as relatives. Therapeutic Intervention: The patient was treated with NSAIDS, antibiotics, anticonvulsant, antiemetic and antacid and physical therapy to help keep muscle strength and flexibility The patient underwent VP shunt head circumference assessed regularly, vital signs hourly, provided vitamins enriched diet as per dietician’s order assisted dressing for drainage and physical therapy. Conclusion: The patient was admitted in A.V.B.R.H in a critical condition with the diagnosis of dandy walker syndrome, after providing the required treatment by the health care team members of hospital the patient condition was improved and satisfactory.

Highlights

Dandy Walker Syndrome is a congenital brain malformation that affects the cerebellum and the fluid filled areas that accompany it
Patient present history: The male patient 8 year old who was apparently admitted in A.V.B.R.H on 18/8/2019 is diagnosed with a known case of dandy walker malformation and came with the complaints of headache since 4 days, fever since 3 days, vomiting since 5 days and 3 episodes of seizures
The early signs of DW couldbe observed in the newborns including macrocephaly, skull enlargement in the occipital area ultrasound in the brain, CT scan or brain MRI is used to diagnose complex Dandy-Walker [7]

Summary

Introduction

Dandy Walker Syndrome is a congenital brain malformation that affects the cerebellum and the fluid filled areas that accompany it. The CT scan as well as MRI reports has shown that large posterior fossa cyst with open communication with fourth ventricle with hypoplastic left cerebellar hemisphere and no visualized cerebellar vermis. The malformation of DandyWalker is a congenital (present at birth) disorder that affects the cerebellum, the back section of the brain that regulates speech, actions and cognitive abilities. Dandy Walker malformation signs usually turn up by age 1year [1]. Those symptoms could include: Developmental motor and language skills delays, such as sitting, Low muscle tone, flexibility and posture Problems with eye movement, jerky eye motion hearing loss, hydrocephalus complicates the majority of

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Discussion

Conclusion