Case 151: Hereditary Angioedema in the Duodenum

Abstract

HomeRadiologyVol. 253, No. 2 PreviousNext Case 151: Hereditary Angioedema in the DuodenumJesse Courtier, Kamran AliJesse Courtier, Kamran AliAuthor Affiliations1From the Department of Radiology, University of Kansas–Wichita, Wichita, Kan.Address correspondence to J.C., 1 St Francis Pl, Room 4606, San Francisco, CA 94107 (e-mail: [email protected]).Jesse CourtierKamran AliPublished Online:Nov 1 2009https://doi.org/10.1148/radiol.2532080598MoreSectionsFull textPDF ToolsImage ViewerAdd to favoritesCiteTrack CitationsPermissionsReprints ShareShare onFacebookTwitterLinked In AbstractTo reach the correct diagnosis of hereditary angioedema, it was necessary to integrate the patient's imaging findings with his clinical and family history, as well as his laboratory data; this case illustrates the necessity of the integration of clinical and radiologic findings, as well as the use of a pattern approach to complex small-bowel processes. References 1 Ghai S, Pattison J, Ghai S, O'Malley ME, Khalili K, Stephens M. Primary gastrointestinal lymphoma: spectrum of imaging findings with pathologic correlation. RadioGraphics 2007;27(5):1371–1388. Link, Google Scholar2 Fishman EK, Kuhlman JE, Jones RJ. CT of lymphoma: spectrum of disease. RadioGraphics 1991;11(4):647–669. Link, Google Scholar3 Macari M, Megibow A, Balthazar E. A pattern approach to the abnormal small bowel: observations at MDCT and CT enterography. AJR Am J Roentgenol 2007;188(5):1344–1355. Crossref, Medline, Google Scholar4 Buckley JA, Fishman EK. CT evaluation of small bowel neoplasms: spectrum of disease. RadioGraphics 1998;18(2):379–392. Link, Google Scholar5 Jayaraman MV, Mayo-Smith WW, Movson JS, Dupuy DE, Wallach MT. CT of the duodenum: an overlooked segment gets its due. RadioGraphics 2001;21(Spec Issue):S147–S160. Link, Google Scholar6 Bork K, Staubach P, Eckardt AJ, Hardt J. Symptoms, course, and complications of abdominal attacks in hereditary angioedema due to C1 inhibitor deficiency. Am J Gastroenterol 2006;101(3):619–627. Crossref, Medline, Google Scholar7 Hertz IH, Keller RJ. Paroxysmal nocturnal hemoglobinuria: small bowel findings. AJR Am J Roentgenol 1981;136(2):204–205. Crossref, Medline, Google Scholar8 Choudhary AM, Grayer D, Nelson A, Roberts I. Mesenteric venous thrombosis: a diagnosis not to be missed! J Clin Gastroenterol 2000;31(2):179–182. Crossref, Medline, Google Scholar9 Byun JY, Ha HK, Yu SYet al.. CT features of systemic lupus erythematosus in patients with acute abdominal pain: emphasis on ischemic bowel disease. Radiology 1999;211(1):203–209. Link, Google Scholar10 De Backer AI, De Schepper AM, Vandevenne JE, Schoeters P, Michielsen P, Stevens WJ. CT of angioedema of the small bowel. AJR Am J Roentgenol 2001;176(3):649–652. Crossref, Medline, Google Scholar11 Pekdemir M, Ersel M, Aksay E, Yanturali S, Akturk A, Kiyan S. Effective treatment of hereditary angioedema with fresh frozen plasma in an emergency department. J Emerg Med 2007;33(2):137–139. Crossref, Medline, Google Scholar12 Fisher AJ, Fleishman MJ, Hancock D. Angioedema of the small bowel: CT appearance. AJR Am J Roentgenol 2000;175(2):554. Crossref, Medline, Google Scholar13 Ciaccia D, Brazer SR, Baker ME. Acquired C1 esterase inhibitor deficiency causing intestinal angioedema: CT appearance. AJR Am J Roentgenol 1993;161(6):1215–1216. Crossref, Medline, Google ScholarArticle HistoryReceived April 1, 2008; revision requested June 2; revision received August 19; final version accepted August 27.Published in print: Nov 2009 FiguresReferencesRelatedDetailsCited ByTherapies, Vol. 75, No. 2La Presse Médicale, Vol. 44, No. 3Rude Awakening: Acute Abdominal Pain with Spontaneous ResolutionThe American Journal of Medicine, Vol. 125, No. 10Recommended Articles CT Findings of Acute Small-Bowel EntitiesRadioGraphics2018Volume: 38Issue: 5pp. 1352-1369Pearls, Pitfalls, and Conditions that Mimic Mesenteric Ischemia at CTRadioGraphics2020Volume: 40Issue: 2pp. 545-561Fluoroscopic Evaluation of Duodenal DiseasesRadioGraphics2022Volume: 42Issue: 2pp. 397-416Imaging Review of Gastrointestinal Motility DisordersRadioGraphics2022Volume: 42Issue: 7pp. 2014-2036Imaging of Drug-induced Complications in the Gastrointestinal SystemRadioGraphics2016Volume: 36Issue: 1pp. 71-87See More RSNA Education Exhibits Gastrointestinal Tract Dilation: How and Why it Happens. A Simplified Review of the Pathophysiologic Mechanisms and CausesDigital Posters2020Non-Neoplastic Diseases of the Small Intestine and Their Pattern of Mural InvolvementDigital Posters2018The Many Faces of Bowel IschemiaDigital Posters2019 RSNA Case Collection Jejunal diverticulitisRSNA Case Collection2021Superior Mesenteric Artery SyndromeRSNA Case Collection2021TrichobezoarRSNA Case Collection2021 Vol. 253, No. 2 Metrics Altmetric Score PDF download