Carney Complex with Multiple Cardiac Myxomas, Pigmented Nodular Adrenocortical Hyperplasia, Epithelioid Blue Nevus, and Multiple Calcified Lesions of the Testis: A Case Report.

Abstract

In 1985, Carney et al. [1] reported a syndrome composed of myxoid tumors, endocrine overactivity, and pigmented skin lesions. Myxoid tumors typically manifested as cardiac myxoma, cutaneous myxoma, and myxoid mammary fibroadenoma. Endocrine overactivity, such as acromegaly and Cushing’s syndrome, presented with associated endocrine tumors, including pituitary adenoma, thyroid tumors, primary pigmented nodular adrenocortical disease (PPNAD), and testicular tumors [2]. Pigmented skin lesions include lentiginosis, conventional melanocytic nevus, and epithelioid blue nevus [3].