Abstract
Purpose :
 We present a-12-year old female with canal stenosis and canal cholesteatoma. We discuss the clinical, radiological and treatment option for canal cholesteatoma in canal stenosis
 Discussion :
 Congenital canal atresia is a failure of the development of the external auditory canal which comprises anomalies of variable severity involving pinna, external acoustic canal, middle ear structures and rarely inner ear leading to hearing impairment. Congenital canal stenosis is considered to be a subset of congenital canal atresia. This malformation results in mild to severe conductive hearing loss. Furthermore, risk of cholesteatoma increased when it is associated with stenotic ear. Radiological evaluation in the form of HRCT scan of temporal bones should always be done in these patients during their initial presentation and surgery should be planned accordingly. Their presence should be rule out prior any corrective surgery.
 Conclusion :
 Although the incidence of canal cholesteatoma is rare in congenital canal stenosis, all patients presenting with canal atresia or stenosis should be evaluated thoroughly due to their potential to develop cholesteatoma as it may be challenging to treat at an advanced stage in view of morbid complications.
Highlights
We present a case of a 12-year-old girl with canal cholesteatoma (CC) with canal stenosis to discuss the clinical, radiological, and treatment options for this disease.Patient: A 12-year-old girl with the right microtia with canal stenosis, who was referred to our center, presented with the right ear discharge for the past 2 years
Congenital canal atresia is a birth defect characterized by hypoplasia of the external auditory canal (EAC) and often associated with microtia or dysmorphic features of the pinna and middle ear with rarely abnormalities of inner ear structures (1)
High-resolution computed tomography (CT) scan of the temporal bone revealed the presence of soft-tissue density in the middle ear with canal stenosis (Figure 1)
Summary
All patients with congenital canal stenosis should undergo a CT scan of the temporal bone at an early age to exclude CC. Hearing assessment is necessary to achieve early intervention, such as canalplasty or bone conduction hearing aid fitting. Key words: Canal cholesteatoma; congenital canal atresia; canal stenosis; hearing loss
Sign-in/Register to view highlights & summary Talk to us
Join us for a 30 min session where you can share your feedback and ask us any queries you have
Schedule a callDisclaimer: All third-party content on this website/platform is and will remain the property of their respective owners and is provided on "as is" basis without any warranties, express or implied. Use of third-party content does not indicate any affiliation, sponsorship with or endorsement by them. Any references to third-party content is to identify the corresponding services and shall be considered fair use under The CopyrightLaw.
