Abstract
ABSTRACTCongenital macrostomia or transverse facial cleft is a rare congenital craniofacial anomaly, which affects the esthetics and functions of oral cavity. It is usually associated with deformities of other structures developed from the first and second branchial arches. Bilateral transverse cleft, occurring alone is uncommon. Since the deformity is rare, its treatment has not been commonly described in the literature. We report a case of congenital bilateral macrostomia as an isolated, asyndromic deformity to add one more case in the literature and surgical technique has been discussed here.
Highlights
Transverse facial cleft (Tassier type 7)[1] or congenital macrostomia is a rare congenital anomaly,[1,2] which results from failure of the maxillary and mandibular portions of the first brachial arch to unite.[3,4]
These clefts mostly occur as part of syndromes such as facial dysostosis and branchial arch
Various surgical techniques like Z-plasty, W-plasty, triangular flaps and straight line closure have been described in the literature with variable success
Summary
Transverse facial cleft (Tassier type 7)[1] or congenital macrostomia is a rare congenital anomaly,[1,2] which results from failure of the maxillary and mandibular portions of the first brachial arch to unite.[3,4] These clefts mostly occur as part of syndromes such as facial dysostosis and branchial arch. Isolated transverse facial cleft is a rarity. The estimated occurrence varies from 1 in 100 to 1 in 300 of all facial clefts.[6] Various etiopathogeneses have been described. According to Mckenzie and Craig.[7] The defects of the first brachial arch arise from inadequate arterial blood supply occurring during a period of rapid and critical facial growth and development.
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