Bilateral Posterior and Lateral Semicircular Canals Aplasia Associated with Other Inner Ear Malformation in A 2-Year-Old Child: A Rare Case Report

Fatimah Albazroun

doi:10.32474/sjo.2018.01.000116

Abstract

Bilateral Posterior and Lateral Semicircular Canals Aplasia Associated with Other Inner Ear Malformation in A 2-Year-Old Child: A Rare Case Report

Highlights

Inner ear in embryo starts to develop during 3rd week of gestation
We report the case of one of the non-identical twin brothers: a 2-year-old boy, born of a consanguineous marriage to medically free parents, was first seen and diagnosed in our institution when he was 1-year-old to have bilateral profound Sensorineural Hearing Loss (SNHL)
The patient has been in regular follow-up at our ENT outpatient department. His parents had not reported any active complains about him up until he started walking, they stated that he had unsteady gait and poor balance which usually followed by Falls or in some occasions ‘a fainting episode’ which they have never noticed with his twin brother

Summary

Introduction

Inner ear in embryo starts to develop during 3rd week of gestation. A structure called ‘otic placodes’ which arise from the surface ectoderm on each side of the rhombencephalon represent the fundamental embryological part of inner air developmental. We report the case of one of the non-identical twin brothers: a 2-year-old boy, born of a consanguineous marriage to medically free parents, was first seen and diagnosed in our institution when he was 1-year-old to have bilateral profound SNHL. His hearing loss was first noticed by his mother when he was five months of age. The patient has been in regular follow-up at our ENT outpatient department His parents had not reported any active complains about him up until he started walking, they stated that he had unsteady gait and poor balance which usually followed by Falls or in some occasions ‘a fainting episode’ which they have never noticed with his twin brother.

Findings

Discussion

Conclusion