Bilateral linear nevus comedonicus on eyelids – A rare presentation

Vijay Zawar,Antonio Chuh,Swati Zawar

doi:10.7241/ourd.20161.12

Abstract

We describe a female child with linear comedone-like lesions over both the eyelids which histologically confirmed Naevus Comedonicus. She only partially responded to topical tretinoin cream. There was no clinically evident overt systemic association in our case.

Highlights

Naevus Comedonicus (NC) is an uncommon developmental defect of the pilosebaceous apparatus characterised by group of slightly elevated papules which have central, dark, firm hyperkeratosis plug resembling a comedo [1]
Widespread cutaneous involvement or giant lesions are exceptional as are the systemic associations such as skeletal defects, cataract, cerebral anomalies [1,5,6] and arterio-hepatic dysplasias (Alagille syndrome) [7]
An 8-years old female child was brought by her parents for asymptomatic “string of black dots” on both of her eyelids noticed since six months which were slowly progressive

Summary

INTRODUCTION

Naevus Comedonicus (NC) is an uncommon developmental defect of the pilosebaceous apparatus (or rarely, may be of the sweat duct) characterised by group of slightly elevated papules which have central, dark, firm hyperkeratosis plug resembling a comedo [1]. It was first described by Kofmann in 1895 [2]. Face, trunk and uncommonly the genitalia [3], palms and soles [4] It is unilateral and an isolated cutaneous defect. Widespread cutaneous involvement or giant lesions are exceptional as are the systemic associations such as skeletal defects, cataract, cerebral anomalies [1,5,6] and arterio-hepatic dysplasias (Alagille syndrome) [7]

CASE REPORT

DISCUSSION