Bilateral adrenal teratomas

Abstract

Abstract Teratoma is a rare type of germ cell neoplasm (GCN) which has an incidence of 0.9/100,000. These tumours occur more frequently in girls than in boys, and they usually are diagnosed before four years of age, with a mean age of 18 months. About 75% of these lesions are benign teratomas. Teratomas usually occur in the ovaries and testes, and less commonly in anterior mediastinum, retroperitoneum, sacrococcygeal region, and intestine. Primary adrenal teratomas are extremely rare, with only 18 cases of primary adrenal teratoma previously reported and only three paediatric cases (youngest age 1 day old). The management of adrenal teratoma is surgical resection. Surgery for mature adrenal teratomas is thought to be curative, but follow-up to monitor reoccurrence is warranted as long-term data are very limited. Bilateral adrenal teratoma has never been reported in the literature. We report a case on a two-year-old boy with bilateral mature adrenal teratoma who underwent successful surgical resections and summarise the related literature.