Abstract
Extra-adrenal paraganglioma of the retroperitoneum are rare neuroendocrine tumors arising from specialized neural crest cells, intimately associated with sympathetic nervous tissue and distributed along the aorta. Here we present a case of multiple extra-adrenal retroperitoneal paraganglioma in a 16-year-old boy. The clinical presentation, imaging characteristics, and surgical pathologic findings were reported. A comprehensive review of the medical literature concerning multiple extra-adrenal paraganglioma in the pediatric and adult population is also discussed.
Highlights
Extra-adrenal retroperitoneal paraganglioma are rare neuroendocrine tumors arising from specialized neural crest cells, intimately associated with sympathetic nervous tissue and distributed along the aorta [1]
The general designation “paraganglioma” applies to tumors arising from paraganglia regardless of location
The only exception is the paraganglioma of the adrenal medulla, which is universally known as pheochromocytoma
Summary
Bi-Focal Retroperitoneal Paraganglioma in a Young Patient: A Case Report and Review of the Literature.
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