Abstract

We are reporting four cases of acquired double orifice mitral valve (DOMV) of rheumatic etiology (rare) presenting as significant mitral stenosis (MS) treated successfully by percutaneous intervention. All four patients are young (3 males, 1 female) who presented with dyspnea of Newyork heart association (NYHA) class II with mean duration of 1.3 years. Typical clinical findings of MS were present in all. Echocardiography confirmed the diagnosis of moderate to severe MS of rheumatic etiology with double orifice of mitral valve of Trowitzsch incomplete bridge variety [1], giving appearance of two equal (like a pair of spectacles in one patient) or unequal size orifices (in three patients) in parasternal short axis view. Color Doppler examination revealed separate jets originating from each orifice, determined severity of the lesion and evaluated the eligibility for balloon mitral valvuloplasty (BMV). BMV was carried out under transeosophagial echo (TEE) guidance (for perfect septal puncture and crossing the separate orifices) using Inoue balloon of appropriate size (in accordance with patient’s height) with intention to break central fibrous strand converting into a single orifice. All four patients underwent successful BMV (clinical & ECHO criteria) after dilating the separate orifices (except case 4) but the fibrous strand could not be broken. Hence, this study shows that good results can be obtained in acquired double orifice mitral valve with significant MS with BMV even without breaking the fibrous strand. Considering rarity of isolated DOMV cases and rheumatic etiology being very rare, this report of four rheumatic acquired DOMV cases with successful BMV done with good result is significant.

Highlights

  • Double orifice mitral valve (DOMV) is an uncommon anomaly that was first described by Greenfield in 1876

  • Acquired double orifice mitral valve stenosis of favourable morphology can be effectively treated with balloon mitral valvuloplasty (BMV) using Inoue balloon under transeosophagial echo (TEE) guidance to reduce the procedure time, to dilate the desired orifice and to reduce the complication

  • Desired fall in the Trans mitral gradient (TMG) should be the goal of the procedure rather than to achieve a single orifice valve

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Summary

Introduction

Double orifice mitral valve (DOMV) is an uncommon anomaly that was first described by Greenfield in 1876. (2015) Balloon Mitral Valvuloplasty in Rheumatic Double Orifice Mitral Valve. Most common cause of DOMV is congenital wherein there is abnormal subvalvular apparatus which leads to separate tendinous insertions and formation of two orifices in mitral valve [1]. It is usually associated with other congenital anomalies like atrioventricular septal defect (AVCD), outflow tract obstructions etc. Percutaneous balloon mitral valvuloplasty is a time tested treatment for rheumatic mitral stenosis since 1984 [9], but for valves with single orifice. The long term outcome for BMV in DOMV is still not known

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