Bacak Ülserleri ve Degos Benzeri Lezyonlar Bulunan Sistemik Lupus Eritematozusun Nadir Bir Sunumu

Abstract

Degos-like lesions (DLL) have been associated with connective tissue diseases. Till date only twelve cases of systemic lupus erythematosus (SLE) with DLL have been published. We describe a rare case of SLE with leg ulcers and DLL. A 23-year-old male presented with malar rash, photosensitivity, leg ulcers, joint pain, oral ulcers, altered sensorium and dyspnea. Cutaneous examination also revealed atrophic, porcelain-white scars over body previously unnoticed by patient. Dermoscopy of atrophic lesions was pathognomonic of Degos disease. Histopathology from various lesions were consistent with Degos disease and SLE. Patient was admitted in intensive care unit but succumbed to multiorgan failure two days later. This case highlights the importance of dermoscopy for immediate diagnosis of DLL. Appropriate investigations for early diagnosis and timely management can decrease mortality. Also a thorough examination in cases of connective tissue diseases may reveal uncommon lesions that can alter clinical course and outcome of patients.