Abstract
Purpose: To describe the extremely rare occurrence of acinic cell carcinoma of the parotid in a young child. Materials & Methods: A 14-year-old boy presented with a left sided facial mass. It was initially thought to be a bug bite or perhaps a wrestling injury. However, it progressed rapidly overall several weeks. CT revealed a well-circumscribed, cystic, 3.9 × 2.8 × 3.2 cmmass centered in the deep lobe of the left parotid gland, also involving the superficial lobe and extending medially through the stylomandibular tunnel with a component extending to the stylomastoid foramen. There was no solid enhancing portion. There were several enlarged level II lymph nodes suspicious for nodal metastases. Results: The mass was biopsied and pathology was consistent with acinic cell carcinoma. Complete left parotidectomy and left selective neck dissection was performed, confirming the diagnosis. Conclusions: Salivary gland neoplasms are rare in children. Less than 5% of salivary gland tumors occur in children. Salivary gland neoplasms account for less than 8% of pediatric head and neck tumors. Approximately 1/3 of salivary gland tumors arising in childhood are malignant; most being mucoepidermoid. Acinic cell carcinoma of the parotid gland in children is extremely rare, especially in those under age 16, with only a few available case reports. This case was also unusual in that the lesion was predominantly cystic.
Highlights
Salivary gland tumors are exceedingly rare in childhood with an annual incidence of this malignancy of 0.8 per million
The mass was biopsied and pathology was consistent with acinic cell carcinoma
Less than 50% of salivary gland malignancies occur in children under the age of 15, and Acinic Cell Carcinoma accounts for about 35% of all salivary gland malignancies [1]
Summary
Salivary gland tumors are exceedingly rare in childhood with an annual incidence of this malignancy of 0.8 per million. The majority are located in the parotid gland. Less than 50% of salivary gland malignancies occur in children under the age of 15, and Acinic Cell Carcinoma accounts for about 35% of all salivary gland malignancies [1]. We present a case of a predominately cystic Acinic Cell Carcinoma of the parotid gland, which presented in a 14-year-old boy
Talk to us
Join us for a 30 min session where you can share your feedback and ask us any queries you have