Assessment of intraatrial lateral tunnel anatomy and venous blood flow in children with hypoplastic left heart syndrome in Fontan circulation

Inga Voges,Traudel Hansen,Hans-Heiner Kramer,Carsten Rickers,Michael Jerosch-Herold,Jens Scheewe,Dominik Daniel Gabbert,Christopher Hart

doi:10.1186/1532-429x-14-s1-p113

Abstract

Background In patients (pts) with hypoplastic left heart syndrome (HLHS) post completion of the total cavopulmonary connection (TCPC) with an intraatrial lateral tunnel, deviations of the tunnel from an ideal tubular shape are common. However, little is known about frequency and potential adverse effects of such shape deviations. Therefore, we sought to analyze intraatrial lateral tunnel anatomy, dimensions and blood flow in children with HLHS with cardiac magnetic resonance imaging (CMR).

Highlights

In patients with hypoplastic left heart syndrome (HLHS) post completion of the total cavopulmonary connection (TCPC) with an intraatrial lateral tunnel, deviations of the tunnel from an ideal tubular shape are common
Sixty-one pts with HLHS underwent 3.0-T cardiac magnetic resonance imaging (CMR) (Achieva 3.0T, Philips Medical Systems) with gradient-echo cine sequences (FOV=280x224 mm, TR/TE=4.4/2.5 ms), 2Dphase-contrast cine imaging (FOV=270x270 mm, TR/ TE=4.4/2.7 ms, VENC=100 cm/s) and flow-sensitive 3D-phase-contrast CMR (FOV=320 mm, TR/TE=3.3/2.2 ms, 12 slices, 25 phases)
Tunnel blood flow was measured at the level below the connection of the inferior vena cava with the pulmonary arteries

Summary

Introduction

In patients (pts) with hypoplastic left heart syndrome (HLHS) post completion of the total cavopulmonary connection (TCPC) with an intraatrial lateral tunnel, deviations of the tunnel from an ideal tubular shape are common. Assessment of intraatrial lateral tunnel anatomy and venous blood flow in children with hypoplastic left heart syndrome in Fontan circulation Background In patients (pts) with hypoplastic left heart syndrome (HLHS) post completion of the total cavopulmonary connection (TCPC) with an intraatrial lateral tunnel, deviations of the tunnel from an ideal tubular shape are common.

Results

Conclusion