Abstract
Ehlers-Danlos syndrome is an inherited disorder of the connective tissue characterized by increased elasticity of the skin, hypermobile joints and fragility of the vascular system. Vascular complications in these patients, requiring surgical repair, can be life-threatening with high perioperative morbidity and mortality. Reports of successful treatment of aortic ruptures or dissections in vascular Ehlers-Danlos syndrome patients are rare. We describe our surgical technique and precautions in an Ehlers-Danlos syndrome patient with a contained rupture of the ascending aorta, requiring emergency surgical intervention.
Talk to us
Join us for a 30 min session where you can share your feedback and ask us any queries you have
Disclaimer: All third-party content on this website/platform is and will remain the property of their respective owners and is provided on "as is" basis without any warranties, express or implied. Use of third-party content does not indicate any affiliation, sponsorship with or endorsement by them. Any references to third-party content is to identify the corresponding services and shall be considered fair use under The CopyrightLaw.