Abstract
Behcet's disease (BD) is a chronic, recurrent, systemic disease that is characterized by oral and genital ulcers and oculocutaneous inflammatory lesions. Cardiovascular involvement especially large artery involvement is a serious and vital complication of BD. Pseudoaneurysms in the major arteries may be the cause of sudden death in BD. In our case a pulsatile abdominal mass was determined to be an aortic pseudoaneurysm associated with BD and an aortocaval fistula. Here we report this case and a short review of literature because this is the first reported aortocaval fistula in a BD patient in English literature.
Highlights
Behcet’s disease (BD) is a well-known autoimmune multisystemic disorder that is characterized by oral and genital ulcers and oculocutaneous inflammatory lesions
We report a rare case of aortocaval fistulae (ACF) and abdominal aortic pseudoaneurysm due to BD in a young male
After opening the pseudoaneurysm pouch and evacuating the thrombus we found the venous bleeding into the aneurysm pouch at the right and distal part of the pseudoaneurysm that was coming from a 0.5 cm connection from the inferior vena cavae
Summary
Behcet’s disease (BD) is a well-known autoimmune multisystemic disorder that is characterized by oral and genital ulcers and oculocutaneous inflammatory lesions. The most important predictor of morbidity and mortality is the vascular complications especially arterial involvement of this disease [1, 2]. The typical vascular presentations are both arterial occlusive and aneurysm formation in the medium and large vessels. The inflammatory obliteration of the vasa vasorum of the arterial wall may lead to perforation or pseudoaneurysm formation. Fistula formation to the inferior vena cava is a rare complication of abdominal aorta aneurysm (AAA). The incidence of aortocaval fistulae (ACF) varies between 0.2% and 0.9% as a complication of AAA [3]. Spontaneous erosion of the aneurysm into the vena cava is the major cause of the primary ACF. Most of these aneurysms are atherosclerotic in nature. We report a rare case of ACF and abdominal aortic pseudoaneurysm due to BD in a young male
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