Aortic root replacement in a patient with congenital hypofibrinogenemia

Abstract

Complex cardiac surgical procedures involving cardiopulmonary bypass increases the risk of bleeding in patients with hypofibrinogenemia. We present a 27-year-old patient, a known case of hypofibrinogenemia, who was diagnosed with a bicuspid aortic valve and dilated aortic root. He underwent an uneventful Bentall procedure with minimal bleeding and bleeding-related complications. We believe that aortic root surgery can be safely performed in a patient with congenital hypofibrinogenemia under the cover of adequate fibrinogen replacement.