Aortic atresia with normal left ventricle and intact ventricular septum—a major form of subaortic stenosis complicating an atrioventricular septal defect with intact septal structures

Abstract

SummaryWe report an unusual form of aortic atresia with a normal sized left ventricle, intact ventricular septum and isolated cleft of the left atrioventricular valve, with abnormal attachments creating both subaortic atresia and massive regurgitation across the left atrioventricular valve. This combination, never described before as far as we are aware, can be considered as an extreme form of subaortic stenosis complicating a very particular type of atrioventricular septal defect.