Angiosarcoma of the Scalp: A Case Report

Bekralas H

doi:10.31579/2578-8868/227

Abstract

Angiosarcomas also called hemangioendothelia, are rare and highly malignant vascular tumors of mesodermal origin, they represent 08-10% of cancers and can affect any part of the body.Angiosarcoma mainly affects the skin, the face is the preferred topography in adults, it remains exceptional in children, with a predilection for the mediastinum and pericardium,The angiogenesis of angiosarcomas is still poorly understood; However, chronic lymphedema and exposure to prolonged radiotherapy are blamed. Total surgical excision is the treatment of choice in localized forms, followed by chemotherapy. pre- and post-operative radiotherapy may be necessary.New studies have shown the effectiveness of beta blockers (propranolol) in the management of angiosarcomas.The prognosis depends on the age of the patient, the size of the tumor, the histological grade and the extent of tumor progression.

Highlights

Cutaneous angiosarcomas are rare, aggressive vascular tumors with a poor prognosis; they represent approximately 1 to 5% of soft tissue sarcomas in adults and 0.2 to 0.3 in children.WILSON – JONES angiosarcoma of the head and neck is a peculiar and exceptional topographic form in children
Materials and methods: We report a rare case of congenital angiosarcoma of the scalp in a newborn 7 days old, referred to our level by his pediatrician following the observation of an occipital lesion which rapidly increases in size
The clinical examination found a conscious newborn, general condition preserved with skin-mucous paleness, in relation to anemia at 7g / dl

Summary

Introduction

Aggressive vascular tumors with a poor prognosis; they represent approximately 1 to 5% of soft tissue sarcomas in adults and 0.2 to 0.3 in children. WILSON – JONES angiosarcoma of the head and neck is a peculiar and exceptional topographic form in children. Congenital or intrauterine forms have been described in the literature

Materials and methods

Conclusion