Abstract

Renal angiomyolipoma is a benign tumor formed by smooth muscle, adipose tissue and blood vessels. It is commonly found incidentally and its clinical manifestations are pain and abdominal mass or spontaneous tumor rupture with retroperitoneal bleeding. The clinical presentation of a hemorrhagic shock secondary to a retroperitoneal hematoma is uncommon. We report a 40 year-old male who presented to the emergency room with lumbar pain and deterioration of hemodynamic parameters. The CT scan showed a left renal injury associated to an expansive retroperitoneal process. The abdominal exploration, vascular control of the renal pedicle and nephrectomy allowed a successful outcome.

Highlights

  • Renal angiomyolipoma is a benign tumor formed by smooth muscle, adipose tissue and blood vessels

  • We report a 40 year-old male who presented to the emergency room with lumbar pain and deterioration of hemodynamic parameters

  • La nefrectomía con control vascular precoz es habitualmente necesaria para detener la evolución irreversible del shock hemorrágico

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Summary

Introduction

Renal angiomyolipoma is a benign tumor formed by smooth muscle, adipose tissue and blood vessels. El angiomiolipoma es un tumor benigno del mesénquima que se compone de músculo liso, tejido adiposo y vasos sanguíneos de pared fina y distribución aberrante de tipo hamartomatoso. El manejo de los angiomiolipomas depende del contexto clínico en el que se presentan. Los tumores asintomáticos diagnosticados de manera incidental requieren seguimiento periódico[2] el crecimiento rápido, el tamaño mayor a 4 cm y el Figura 1: TAC de abdomen y pelvis que muestra lesión del riñón izquierdo y ocupación del retroperitoneo.

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