Anesthetic management of a pregnant patient with multiple pterygium syndrome (Escobar type)

Abstract

Multiple pterygium syndrome is a rare disorder with several subtypes. Its features include pterygia (excessive webbing), arthrogryposis (congenital contractures), ankyloglossia (adhesions of the tongue to the palate), syngnathia (congenital bands of tissue between the maxilla and mandible), cleft palate, micrognathia, scoliosis, short stature, craniofacial dysmorphism, arachnodactyly and congenital respiratory distress.1 The Escobar subtype includes webbing of the neck that increases with age, lumbar lordosis and webbing of the elbows and knees that develops before adolescence.