Anesthetic management of a patient with restrictive cardiomyopathy and ebstein anomaly for femoral hernia repair

Abstract

Ebstein anomaly along with restrictive cardiomyopathy is a rare entity characterized by apical displacement of the septal and posterior tricuspid valve leaflets, leading to atrialization of the right ventricle with a variable degree of malformation and displacement of the anterior leaflet along with the restriction of diastolic filling of ventricles. If patients with this anomaly present to us along atrial fibrillation and liver dysfunction due to right-sided heart failure, it would be a challenge for anesthesiologist to give anesthesia. Herein, we are providing a brief review of the clinical presentation and anesthetic consideration in these types of patients if they present for noncardiac surgeries.