Anesthetic Management for Dental Procedures of a Child with Frank-ter Haar Syndrome

Abstract

Frank-ter Haar syndrome is a very rarely encountered genetic disorder. Multiple skeletal abnormalities and abnormal facial features of these patients cause an increase in difficult intubation. This report presents our experience of a pediatric female patient with a difficult airway due to her Frank-ter Haar syndrome features. Patient repeatedly underwent two different dental procedures, under sedation and general anesthesia. The patient was prepped with soft cushions during operations. Intraoral secretions, bleeding and irrigation solutions were carefully suctioned during sedation. Another precaution taken was the disuse of muscle relaxant. Videolaryngoscope was another consideration used for the difficult intubation case. Both procedures were finalized without complications. Frank-ter Haar syndrome patients require wider range of planning and preparation in order to provide comfort and success.