Anesthetic Management for a Patient of Gorham’s Syndrome: The Vanishing Bone Disease

Megumi Harima,Eisuke Kako,Aiji Sato-Boku,Jun Harada,Kazuya Sobue

doi:10.4236/ojanes.2017.76015

Abstract

Gorham-Stout (GS) syndrome or the vanishing bone disease is a very rare chronic disease characterized by the destruction of the osseous matrix and proliferation of vascular structures. Review of the general anesthesia showed only a few cases till date. We report general anesthesia for tooth extraction in a 21-year-old male patient with Gorham-Stout syndrome. In this case, the most concerning issue was limited mouth opening due to mandible osteolysis and difficult intubation was anticipated. To anticipate difficult airway management, it is very important to consider the preoperative airway assessment including the cervical spine screening. In this case, the McGrath video laryngoscope prevented the anticipated difficult intubation due to the limited mouth opening due to mandible osteolysis.

Highlights

Gorham-Stout (GS) syndrome or the vanishing bone disease is a very rare chronic disease characterized by the destruction of the osseous matrix and proliferation of vascular structures
We report general anesthesia for tooth extraction in a 21-year-old male patient with Gorham-Stout syndrome
We describe the anesthetic management of a 21-year-old male with GS syndrome, who was scheduled for tooth extraction under general anesthesia

Summary

Introduction

Gorham-Stout (GS) syndrome or the vanishing bone disease is a very rare chronic disease characterized by the destruction of the osseous matrix and proliferation of vascular structures. The syndrome affects one or multiple bones of the patients, including the skull, the upper and lower extremities, the spine and pelvis. The clinical presentation of a patient suffering from vanishing bone disease includes, pain, functional impairment and swelling of the affected region [1]. We describe the anesthetic management of a 21-year-old male with GS syndrome, who was scheduled for tooth extraction under general anesthesia. In this case, the most concerning issue was limited mouth opening due to mandible osteolysis and difficult intubation was anticipated

Case Report

Discussion

Conclusion