Anesthetic implications in Poland syndrome

Abstract

: Poland Syndrome (PS) is a rare birth defect described as unilateral absence of pectoralis major, pectoralis minor, serratus anterior and external oblique muscles and upper limb anomalies. It is also associated with variable thoracic muscle, chest wall and lower limb deformities. Dextrocardia, diaphragmatic hernia, liver and GIT anomalies, renal agenesis have also been reported in literature. In addition, there is association of PS with patient’s susceptibility to malignant hyperthermia (MH). For patients requiring general anesthesia, special preparation and execution are recommended.We share our anesthesia management in a child with PS posted for ear reconstruction and described that patients with PS requires special preparation and attention in intraoperative and post-operative period. In patients of PS requiring general anesthesia adequate preparation must be made keeping in mind not only the anatomical changes but also the much higher possibility of MH in such patients.