Anesthesia management of radiofrequency ablation in a pediatric patient of ebstein anomaly with wolff–Parkinson–White syndrome

Abstract

Ebstein anomaly (EA) is a congenital malformation with an incidence of 0.72/10,000 populations. It is characterized by abnormal displacement of tricuspid valve, atrialization of proximal portion of the right ventricle, right atrial enlargement, and tricuspid valve regurgitation. Twenty percent of patients with EA are associated with Wolff–Parkinson–White syndrome (WPW syndrome). WPW syndrome is a preexcitation syndrome characterized by abnormal accessory pathway between atria and ventricles which can cause perioperative life-threatening arrhythmias such as atrial fibrillation and paroxysmal supraventricular tachycardia. Here, we describe the successful anesthesia management of electrophysiological study with three-dimensional mapping and radiofrequency ablation procedure in an 8-year-old child of EA with WPW syndrome under general anesthesia.