Anestesia para um doente sem dor

Abstract

Congenital insensitivity to pain with anhidrosis or hereditary sensory and autonomic neuropathy type IV is a rare autossomic recessive disorder caused from loss of unmyelinayted nociceptive afferents and innervation to the sweat glands. The patient’s inability to perceive pain leads to recurrent self-inflicted injuries that result in numerous surgeries during their lifetime. Due to its rarity, there is a limited amount of information concerning the anesthetic management of these individuals. Therefore, with this report we aim to describe the case of an infant with congenital insensitivity to pain with anhidrosis who underwent surgical debridement of a wound, to discuss the characteristics of this disease with anesthetic relevance and to compare our choices with the ones in international literature.