Abstract
Sturge-Weber syndrome is a rare syndrome present at birth, characterized by port-wine stain birthmark on face and associated with nervous system and ocular problems. 1 We report a case of a 15 year old girl who presented for trabeculectomy for uncontrolled glaucoma. She was diagnosed to have Sturge-Weber syndrome. General anaesthesia was given for the procedure. Perioperative anaesthetic management is presented in this case report.
Highlights
Sturge-Weber syndrome (SWS) is congenital vascular disorder of unknown etiology. It manifests as facial angioma or leptomeningeal angioma
The facial angioma can involve eye structures leading to refractory glaucoma, which require surgical treatment
The leptomeningeal angioma is associated with progressive neurological symptoms, such as seizures, hemiparesis, and mental retardation.[2]
Summary
Sturge-Weber syndrome (SWS) is congenital vascular disorder of unknown etiology. It manifests as facial angioma or leptomeningeal angioma. Vascular angioma involving airway may lead to difficulty in laryngoscopy and intubation. Case report A 15 years old girl who weighed 41kg, and was a known patient with SWS, presented with glaucoma, which was refractory to medical therapy. She was planned for a trabeculectomy procedure under general anaesthesia. She had a history of convulsions from birth up to age of 3 years. She was currently not on anticonvulsant therapy and a salbutamol inhaler for occasional wheezing She was on oral acetazolamide 250mg twice a day and timolol eye drops twice a day for glaucoma. The patient’s recovery was uneventful and she was discharged from the hospital on 2nd postoperative day
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