An Unusual Presentation of Congenital Esophageal Stenosis Due to Tracheobronchial Remnants in a Newborn Prenatally Diagnosed with Duodenal Atresia.

Cindy Mai,Dirk Van Raemdonck,Gert De Hertogh,Luc Breysem,Maria-Helena Smet

doi:10.5334/jbr-btr.881

Cindy Mai, Dirk Van Raemdonck + Show 3 more

Open Access

https://doi.org/10.5334/jbr-btr.881

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Abstract

Congenital esophageal stenosis due to tracheobronchial remnants is defined as an intrinsic stenosis of the esophagus caused by congenital architectural abnormalities of the esophageal wall. Although CES is present at birth, it remains asymptomatic till at the age of 4–10 months, when solid food is introduced. Here we present a case diagnosed in the neonatal period after urgent cesarean for an associated duodenal atresia complicated with perforation. There is a mutual association between duodenal atresia and congenital esophageal stenosis. When duodenal atresia is diagnosed, think of possible associated esophageal abnormalities, especially when duodenal atresia is complicated by gastric perforation prenatally.

Highlights

Congenital esophageal stenosis due to tracheobronchial remnants (CES-TBR) is defined as an intrinsic stenosis of the esophagus caused by congenital architectural abnormalities of the esophageal wall [1]
These abnormalities in the esophageal wall are assumed to be caused by an error in the separation of the foregut into the trachea and the esophagus [2, 3], as in esophageal atresia with or without tracheoesophageal fistula
We present a case diagnosed in the neonatal period after urgent cesarean for an associated duodenal atresia complicated with perforation

Summary

CASE REPORT

Cindy Mai*, Luc Breysem*, Gert De Hertogh*, Dirk Van Raemdonck* and Maria-Helena Smet*. Congenital esophageal stenosis due to tracheobronchial remnants is defined as an intrinsic stenosis of the esophagus caused by congenital architectural abnormalities of the esophageal wall. CES is present at birth, it remains asymptomatic till at the age of 4–10 months, when solid food is introduced. We present a case diagnosed in the neonatal period after urgent cesarean for an associated duodenal atresia complicated with perforation. There is a mutual association between duodenal atresia and congenital esophageal stenosis. When duodenal atresia is diagnosed, think of possible associated esophageal abnormalities, especially when duodenal atresia is complicated by gastric perforation prenatally

Introduction

Discussion

Remnants in a Newborn Prenatally Diagnosed with Duodenal Atresia