An unusual postextraction hemorrhage associated with Klippel-Trenaunay-Weber syndrome

Abstract

nosed at birth or in the first few years of life, and most cases are sporadic. The syndrome is thought to be caused by a genetic mutation of an autosomal dominant or recessive gene. The anomaly in this syndrome is usually manifested first in the extremities, with the lower extremities much more frequently affected than the upper ones. Other sites of occurrence are the skin, viscera, or craniofacial region, including the oral cavity. Such lesions tend to bleed easily because of the fragility of the blood vessels. 2 Although there have been many reports of KTWS in the oral region, there are very few reports on problems with tooth extraction associated with KTWS. We report a case with prolonged postextraction bleeding resulting in disseminated intravascular coagulation (DIC).