An interesting case of facial en coup de sabre presenting with optic neuritis in the contralateral eye: A rare presentation

Abstract

Ocular involvement in morphea or en coup de sabre (ECS) is relatively infrequent, observed in approximately 2–3% to 14% of cases. The intricate pathogenesis underlying these ocular manifestations remains elusive. Within this context, we present a rare case in a young female patient, wherein, ECS manifested with optic neuritis in the eye contralateral to the linear scleroderma lesion, a phenomenon, hitherto, unreported in the literature. This unique case affirms the importance of comprehensive ophthalmological evaluations, not only at the initial presentation but also in the ongoing care of ECS patients. The recommendation is particularly emphasized in instances where patients perceive the emergence of new ocular symptoms. This approach aims to enhance our understanding of the ocular complexities associated with ECS and improve the overall management of this intriguing condition.