An educational operative image of an extreme form of hypoplastic left heart syndrome

Abstract

Hypoplastic Left Heart Syndrome (HLHS) represents a rare disease but still common mostly in Middle East and East world population. A large fenotype spectrum, ranging from the less severe mitral and aortic stenosis form to the more severe aortic and mitral atresia one, encompass the disease. We present here a clinical case of aortic and mitral atresia fenotype and show an operative image of the extreme form of that disease. A baby 2 d.o. 2.97 Kg has been admitted with an antenatal diagnosis of Hypoplastic Left Heart Syndrome to our Centre.