Amelogenesis Imperfecta – Case Series and Management

Abstract

Amelogenesis imperfecta (AI) incorporates an assemblage of hereditary diseases that involve the defective formation or calcification of enamel. Also known by varied names such as Hereditary enamel dysplasia, Hereditary brown enamel, Hereditary brown opalescent teeth, this defect is entirely ectodermal, since mesodermal components are unaffected. AI is typically characterized by generalized enamel defects in both primary and permanent dentition. The AI trait can be transmitted by either autosomal dominant, autosomal recessive, or X-linked modes of inheritance.AI has a marked impact on aesthetics, function and psychology of the patient. Early intervention and dental rehabilitation should be carried out with strong emphasis on the preventive care and strict follow up schedule. Key words: Amelogenesis imperfecta, developmental anomaly, Dental Rehabilitation