Alveolar Soft Tissue Sarcoma: A Case Report and Literature Review

A M Abdoulwahab,A S Zirbine,M Koini,S K Akambi,Z Konguise,B S Souna

doi:10.4236/ojo.2017.712043

Abstract

Soft alveolar sarcoma is a rare tumor (0.5% to 1% of soft-tissue sarcomas) of poor prognosis that often affects the young subject, with a moderate male predominance. The authors present the diagnostic and therapeutic course of a 60-year-old patient from Niger with no particular previous history, consulted for a painless swelling of the right arm evolving for 6 months, in which the diagnosis of alveolar sarcoma of the soft parts of the arm was selected. A monobloc surgical excision decision was made, with the anatomy and function of the limb retained, with the filling of the area resected with cement and fixed by a locked nail. A conventional three-course chemotherapy regimen was instituted. Alveolar sarcoma of the soft tissues is a rare tumor whose imagery remains unclear, but the diagnosis is based on surgical excision with histopathological examination and immunohistochemical analysis.

Highlights

IntroductionAlveolar sarcoma of the soft tissues is a rare tumor (0.5% to 1% of the soft-tissue sarcomas) of poor prognosis, which often affects the young subject, with a moderate male predominance [1] [2] (surgeon, radiologist, oncologist, radiotherapist and anatomopathologist), but wide surgical excision remains the best therapeutic option
Alveolar sarcoma of the soft tissues is a rare tumor (0.5% to 1% of the soft-tissue sarcomas) of poor prognosis, which often affects the young subject, with a moderate male predominance [1] [2], but wide surgical excision remains the best therapeutic option
Soft alveolar sarcoma is a rare tumor (0.5% to 1% of soft-tissue sarcomas) of poor prognosis that often affects the young subject, with a moderate male predominance

Summary

Introduction

Alveolar sarcoma of the soft tissues is a rare tumor (0.5% to 1% of the soft-tissue sarcomas) of poor prognosis, which often affects the young subject, with a moderate male predominance [1] [2] (surgeon, radiologist, oncologist, radiotherapist and anatomopathologist), but wide surgical excision remains the best therapeutic option.

Clinical Case

Discussion

Findings

Conclusion