Alveolar Soft-Part Sarcoma

Abstract

ALVEOLAR soft-part sarcoma (ASPS) is a rare, aggressive malignancy of uncertain histologic origin seen in young adults. It comprises 0.5-1 % of all soft tissue sarcomas. Usual age of presentation is 15-35 years and site is lower extremities in adults and head and neck in infants and children. It is a slowly growing tumor, however vascular emboli are common and metastasis to the lung or brain may be the first manifestation of the disease. Characteristic cytological features corelate well with histology.