Abstract
BackgroundHere we report a very rare entity of an infratemporal region aggressive fibromatosis in a 23-year-old Tharu man who had presented with the symptoms of painless but progressive trismus.Case presentationWe describe a case of aggressive fibromatosis in a 23-year-old Tharu man. Radiological imaging as well as an immunohistochemistry panel from a biopsy indicated a diagnosis of an aggressive fibromatosis. Since there was no aggravation in his trismus following surgery and because of his poor socioeconomic status, he was advised to attend regular follow-up visits without any adjuvant therapy.ConclusionsThis case report adds to the notion of keeping the differential diagnosis of an aggressive fibromatosis in all patients presenting with progressive but painless trismus. The characteristic imaging findings as well an immunohistochemistry panel will help us clinch the correct diagnosis.
Highlights
BackgroundAggressive fibromatosis (AF) is a very rare entity [1]. Its origin in the infratemporal region presenting solely as trismus is even rarer with only a few cases reported to date [2–5]
We report a very rare entity of an infratemporal region aggressive fibromatosis in a 23-year-old Tharu man who had presented with the symptoms of painless but progressive trismus
We describe a case of Aggressive fibromatosis (AF) in a 23-year-old Tharu man; diagnosis followed detailed radiological imaging as well as an immunohistochemistry (IHC) panel
Summary
Aggressive fibromatosis (AF) is a very rare entity [1]. Its origin in the infratemporal region presenting solely as trismus is even rarer with only a few cases reported to date [2–5]. We describe a case of AF in a 23-year-old Tharu man; diagnosis followed detailed radiological imaging as well as an immunohistochemistry (IHC) panel. This case report highlights the importance of considering this lesion for any patient presenting with progressive, painless, trismus with radiological imaging revealing loss of musculoaponeurotic planes within the infratemporal fossa along the pterygoid muscles. Computed tomography (CT) and magnetic resonance imaging (MRI) revealed an ill-defined lesion in his right infratemporal region extending to the pterygopalatine fossa and the maxillary sinus He has been on regular follow up with no deterioration in his symptoms in the last 4 months His mouth opening improved to three finger width. Our patient had been advised to start weekly methotrexate therapy but he denied it citing their poor economic status
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