Afectación respiratoria en las enfermedades inmunomediadas sistémicas. Enfermedad pulmonar intersticial difusa y enfermedades autoinmunes sistémicas

Abstract

Diffuse interstitial lung diseases (DILD) comprise a heterogeneous set of diseases of different etiologies. Among them, one of the most important groups for their severity and frequency are DILD secondary to systemic autoimmune diseases. Connective tissue diseases (CTD), or connectopathies, are a group of diseases with an autoimmune basis with systemic repercussions. DILD appears with a varying frequency in each of them, although when it does, it tends to have important implications on the severity of the symptoms and prognosis. In this update, we will attempt to explain the different types of DILD, in its inflammatory and predominantly fibrotic forms, that emerge secondarily to the main types of known CTD as well as their diagnostic and therapeutic approach.