Abstract
Undifferentiated embryonal sarcomas of the liver are extremely rare cases in adults. We report the case of a 30-year-old male who presented with early satiety and abdominal pain due to a massive tumor originating from the left liver and occupying the entire epigastrium. The patient underwent bland embolization in an attempt to decrease the size of the tumor. He then underwent a formal left hepatectomy with resection of liver segments 2, 3, and 4. Extrahepatic inflow control of the portal vein and hepatic artery was performed prior to parenchymal transection. No Pringle maneuver was required. Pathology analysis showed a 45 cm tumor consistent with an undifferentiated embryonal sarcoma and negative microscopic margins. The epidemiology, treatment, and prognosis of this unusual cancer presentation are reviewed.
Highlights
Undifferentiated embryonal sarcoma (UES) of the liver is typically an aggressive childhood tumor with poor prognosis
The first review of this pathology was done by Stocker and Ishak in 1978, where it was found that most cases were in children six to ten years of age with no predilection for gender and involving the right lobe in 90% of the cases [1]
UES of the liver are rare and highly malignant childhood tumors, with few cases reported in adults, more commonly found in adult females and in the right lobe [4]
Summary
Undifferentiated embryonal sarcoma (UES) of the liver is typically an aggressive childhood tumor with poor prognosis. The first review of this pathology was done by Stocker and Ishak in 1978, where it was found that most cases were in children six to ten years of age with no predilection for gender and involving the right lobe in 90% of the cases [1]. This rare tumor predominantly affects children, it has been reported in adults [2, 3]. We present a case of a massive UES of the liver in an adult male, highlighting the clinical presentation, pathological findings, and surgical management
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