Acute Esophageal Necrosis (AEN) - A Rare Syndrome: Report of a Case in a Patient with an Underlying Malignancy and Review of the Literature

Barranco Cao Raquel,Ortega Ruipérez Carolina,Molina Mercedes,Herrera María,Zenzola Víctor,Garzón Carlos

doi:10.31487/j.cor.2020.03.11

Abstract

Acute Esophageal Necrosis (AEN) is a rare medical disorder characterized by a diffuse circumferential black esophageal mucosa. The majority of patients present with signs of upper gastrointestinal bleeding. Diagnosis is based on esophagogastroduodenoscopy. Treatment consists of intravenous fluids, proton pomp inhibitors and treatment of the underlying illness. We report a case of acute necrotizing oesophagitis (AEN) with an underlying malignancy.

Highlights

Acute esophageal necrosis (AEN), known as black esophagus and necrotizing esophagitis, is a severe form of acute esophagitis which endoscopy shows a dark, black-appearing color (“black esophagus”) [13]
We report a case of acute necrotizing oesophagitis (AEN) with an underlying malignancy
Acute esophageal necrosis (AEN) is a rare medical disorder characterized by diffuse circumferential black esophageal mucosa

Summary

Introduction

Acute esophageal necrosis (AEN), known as black esophagus and necrotizing esophagitis, is a severe form of acute esophagitis which endoscopy shows a dark, black-appearing color (“black esophagus”) [13]. Anemia should be corrected by red blood cell transfusion In some cases it could be necessary an early surgical intervention when esophageal perforation is suspected [16]. A 52 years-old female, with past medical history of Wolf-ParkisonWhite syndrome and an uterine fibroid surgery had a diagnosis of Ewing sarcoma in April 2018 She had a pelvic mass and bone metastasis includind the second dorsal vertebra (D2) with spinal involvement and dorsal pain of strong intensity. The patient was discharged in a stable condition with parenteral home nutrition Three weeks later she had an upper GI and small bowel series that showed normal passage of oral contrast through the esophagus with smooth mucosa and normal caliber except for a narrowing zone in upper thoracic esophagus (Figure 2).

Findings

Discussion

Conclusion