Abstract

Acrocephaly, or tower head, is the term applied to that syndrome consisting of a dome-shaped skull, with characteristic Roentgen-ray findings, exophthalmos and optic nerve changes, associated with some minor abnormalities, such as a high, arched palate and deformities of the hands or feet. Acrocephaly is synonymous with thurmschadel, Spitzkopf , steeple head, turret skull, turritum caput , tete a la thersite. When combined with deformities of the hands or feet the name acrocephalosyndactilysm is applied. Previous to 1911 Fletcher 1 found there had been reported between eighty and ninety cases. Von Graefe 2 in 1866 first definitely recognized and described the condition. Since then Michel, 3 J. Hirschberg, 4 Enslin, 5 Patry 6 and others have reported cases. The etiology is obscure. The most probable cause is a premature ossification of the cranial sutures, but the underlying cause is unknown. There is not even a good theory. Syphilis does not seem to

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