Absent Pulmonary Valve in Corrected Tetralogy of Fallot

Abstract

We present the case of a 24-year-old male patient with a history of correction of tetralogy of Fallot when he was 2. He reports presenting 6 syncopal episodes during the last 6 months. Therefore, a transthoracic color Doppler echocardiogram was performed, reporting right ventricular dilatation, mild global deterioration of the right ventricular systolic function, absent pulmonary valve with severe insufficiency, and free passage. A diagnosis of absent pulmonary valve with severe valvular insufficiency was made. Surgical treatment was performed by placing an aortic bioprosthesis (stentless) No. 25, Medtronic FreestyleTM, in the pulmonary position. The patient evolved favorably and was discharged without complications on the fourth postoperative day. In addition, a brief bibliographic review of the disease is made.