A010 Transposition of the Great Arteries in the 3DHB Region

Abstract

Transposition of the great arteries (TGA) is a complex congenital heart problem that requires regular monitoring in Adult Congenital Heart Disease (ACHD) clinics. We wanted to assess the demographics of our patients, their outcomes, and their follow up, compared to international monitoring guidelines. We retrospectively collected data for patients >16 years old with TGA in the 3DHB region, utilising the electronic health record. We recorded demographics and outcomes and the frequency of monitoring, from 2010 to 2019, compared with monitoring recommendations from the 2018 American College of Cardiology Guidelines (ACC) for management of ACHD. 52 adults were identified with TGA. The mean age was 29 years (range 17 to 56), with 16 (31%) female. 46 had D-TGA, with 34 having an arterial switch (ASO), 10 an atrial switch, and 2 a Rastelli procedure as their initial surgery. 6 women had a total of 9 successful pregnancies. In assessing the adequacy of monitoring, patients were seen by a cardiologist within the recommended time frame 62% of the time. The ACC ACHD imaging frequency guidelines were met 50% of the time. However, exercise testing in TGA with ASO (6%) and holter monitoring in D-TGA with atrial switch (0%), were significantly underperformed. Patients with TGA within 3DHB have demographic features similar to other cohorts. The monitoring of our patients is deficient in a number of areas and the information will allow us to address these deficiencies and adjust our follow up accordingly.