A variant of Zinner syndrome presenting with terminal hematuria: A case report

Abstract

Introduction. Zinner syndrome is a rare congenital malformation characterized by ipsilateral renal agenesis or hypoplasia, seminal vesicle cysts, and ejaculatory duct obstruction. Patients are usually asymptomatic or develop unspecific symptoms. Case Report. We present a case of a 22-year-old male patient who presented with painless terminal hematuria. The patient denied trauma or other urinary tract symptoms. Magnetic resonance imaging of the abdomen and pelvis revealed a right renal hypoplasia, a tortuous dilated right ureter draining into polycystic right seminal vesicle, and a dilated ejaculatory duct. Conclusion. The size of the seminal vesicle cyst and symptoms affect the treatment. Asymptomatic cysts may be treated conservatively, while cysts that cause symptoms are often an indication for surgical treatment, due to the possibility of infertility caused by the obstruction of the ejaculatory canal. Magnetic resonance imaging has high-resolution properties providing excellent presentation of anatomical relationships and pathology which is extremely important in case of the need for surgical treatment.