Abstract
Two common treatment options for congenital pseudarthrosis of the tibia (CPT) are intramedullary fixation following resection/shortening of the pseudarthrosis site and reconstruction with an Ilizarov external fixator following resection. We present in detail a narrative of two cases with similar degrees of tibial dysplasia associated with NF-1 treated using these different methods and followed to completion. Technical issues and details of the treatment methods from case reports are discussed in depth. The eventual profoundly different outcomes are correlated to the technical variations used. Treatment with the Charnley-Williams rodding method and aggressive bone grafting supplemented by rh-BMP2 resulted in a normal functioning limb at maturity, while treatment with first, an ineffective version of IM rodding, followed by two sessions of bone transport using an Ilizarov fixator failed to gain useful union and eventually resulted in amputation. Technical details, heretofore inadequately reviewed in the literature, are crucial to the success of either of these commonly utilized treatment methods for CPT.
Highlights
Two common treatment options for congenital pseudarthrosis of the tibia (CPT) are intramedullary fixation following resection/shortening of the pseudarthrosis site and reconstruction with an Ilizarov external fixator following resection
In an attempt to delineate important and crucial treatment principles of two of these methods, we present in detail the following two cases of CPT, which initially appear to be essentially identical lesions but were treated using different methods
Placed in a long leg cast, there was no progress toward union after a 3-month period of immobilization; so, at the age of 1 year, she underwent a type-C procedure [1] consisting of resection of the tibial pseudarthrosis site and placement of a Williams rod with
Summary
Two common treatment options for congenital pseudarthrosis of the tibia (CPT) are intramedullary fixation following resection/shortening of the pseudarthrosis site and reconstruction with an Ilizarov external fixator following resection. Placed in a long leg cast, there was no progress toward union after a 3-month period of immobilization; so, at the age of 1 year, she underwent a type-C procedure [1] consisting of resection of the tibial pseudarthrosis site and placement of a Williams rod with
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