A Rare Malignancy in an Adolescent: Desmoplastic Small Round Cell Tumor

Abstract

Desmoplastic small round cell tumor (DSRCT) is a very rare condition. The peritoneal cavity is most frequently involved. Abdominopelvic computed tomography findings include omental or serosal masses, a dominant tumor, tumor calcification, liver metastasis, abdominal lymphadenopathies, acid and intestinal obstruction. A complete surgical resection including systemic implants, systemic chemotherapy and radiotherapy, hyperthermic intraperitoneal chemotherapy and stem cell transplantation can be used in the treatment of the disease. Since this tumor is very rare, we could only find case reports or a few large numbered patient series in the literature. Here in this case report, we aim to discuss the imaging findings of an adolescent patient at the time of admission.