A rare cause of dilated cardiomyopathy, the left coronary artery from the pulmonary artery (ALCAPA): Accurate diagnosis with dual-source CT

Abstract

An anomalous origin of the left coronary artery (LCA) from the pulmonary artery (ALCAPA syndrome) or Bland–White–Garland syndrome is a rare congenital cardiac anomaly. This syndrome is a rare cause of dilated cardiomyopathy. We report an 8-year-old male patient who presented with intermittent atypical substernal discomfort and mild exertional dyspnea. Dual Source CT and Coronary angiography demonstrated the dilated left atrium and left ventricle with consistent dilated cardiomyopathy and the right coronary artery (RCA) arising from the aorta, rich collaterals from the RCA to LCA and the LCA originated from the pulmonary trunk.