Abstract
BackgroundCongenitally corrected transposition of great arteries (CCTGA) is caused by atrioventricular and ventriculoarterial discordance. Cases of CCTGA with spontaneous chordae rupture of tricuspid valve have not been reported before.Case presentationHere we diagnosed a 38-year-old man, who was found CCTGA 14 years ago, as spontaneous chordae rupture by real-time three dimentional transesophageal echocardiography (RT-3D-TEE). The present case is the first report to describe a CCTGA patient combine with spontaneous chordae rupture in tricuspid valve. After tricuspid valve replacement, the patient was uneventful after 6 years’ follow-up.ConclusionWe reported a rare case with spontaneous chordae rupture of tricuspid valve in a CCTGA patient and explored its etiology here. RT-3D-TEE is an important supplement to 2-dimentional transthoracic echocardiography and can provide more accurate detections in tricuspid valve diseases in CCTGA.
Highlights
Corrected transposition of the great arteries (CCTGA) only occurs in 0.5% of patients exhibiting congenital heart defects
Because tricuspid valve (TV) repair was difficult in TV prolapse with chordae rupture and late results of valvuloplasty were poor in corrected transposition of great arteries (CCTGA), [2] we thought TV replacement was more suitable for this patient and performed TV replacement surgery
In CCTGA, the TV is located within the systemic ventricle, resulting in ability of TV insufficiency
Summary
Corrected transposition of the great arteries (CCTGA) only occurs in 0.5% of patients exhibiting congenital heart defects. Case presentation A 38-year-old male was referred to our hospital because of progressive exertional dyspnea and fatigue of 1 week He was diagnosed as CCTGA in a physical examination without any symptoms 14 years ago. TV regurgitation was mild and ejection fraction (EF) of systemic ventricle was 67% at that time He denied prior history of hypertension, coronary heart disease and diabetes. A short rod-like structure was seen on the left atrial side of TV It swung back and forth with the flow of blood, causing a wide gap in the three valves of TV in systolic period Because TV repair was difficult in TV prolapse with chordae rupture and late results of valvuloplasty were poor in CCTGA, [2] we thought TV replacement was more suitable for this patient and performed TV replacement surgery.
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