A rare case of recurrent pyogenic liver abscess since childhood: A case of Papillon-Lefèvre syndrome

Abstract

Recurrent pyogenic liver abscess since childhood is an uncommon finding in clinical medicine. Papillon-Lefevre syndrome (PLS) is a rare disease characterized by skin lesions caused by palmar-plantar hyperkeratosis, and severe periodontal destruction involving both the primary and permanent dentitions. Till date, more than 200 cases have been reported worldwide. In addition to the skin and oral findings, patients may have immune suppression and an increased susceptibility to bacteria, associated with recurrent pyogenic infections of the skin. Pyogenic liver abscess is an uncommon presentation of this rare syndrome. We present a case of PLS presenting as recurrent pyogenic liver abscess since childhood.