A rare case of persistent urogenital sinus in an adult woman associated with unilateral rudimentary horn with ipsilateral renal agenesis and contralateral dermoid cyst

Mohamed Ibrahim Amer

doi:10.53986/ibjm.2021.0044

Abstract

Persistent urogenital sinus (PUGS) is an uncommon developmental cloacal anomaly, with Incidence of 0.6 in 10000 female births. Herein we depict the case of a 22-year of age lady who presented with Infertility for 16 months with dyspareunia and was found to have Persistent urogenital sinus associated with other urogenital anomalies as unilateral rudimentary horn with ipsilateral renal agenesis and contralateral dermoid cyst. The patient was successfully treated with the excision of the sinus, the rudimentary horn and the dermoid cyst.

Highlights

Urogenital sinus happens because of the arrested migration of the Mullerian ducts from the Muller tubercle to the vestibule [1]
Examination of external genitalia, voiding cystouretherogram, genitoscopy and genitography affirm the presence of persistent urogenital sinus with urinary retention in uterus and vagina [6]. This anomaly is uncommon, with Incidence of 0.6 in 10000 female births and is associated with a wide variety of syndromes. It is a common communication of vagina and urinary tract anywhere from urethral meatus to bladder, and they exit in the perineum as a solitary opening
A short urogenital sinus with an almost normal vaginal vestibule and low urethral opening will happen if the arrest happens late in development, similar to the current case

Summary

INTRODUCTION

Urogenital sinus happens because of the arrested migration of the Mullerian ducts from the Muller tubercle to the vestibule [1]. Urogenital sinus anomalies are characterized by the intersection of the urethra and vagina to frame a common channel of differing length with a solitary perineal opening. Persistent Urogenital Sinus (PUGS) can be grouped into high and low peculiarities as per the length of the common channel (>3 cm or >3 cm, separately). The presence of a urogenital sinus addresses a transient period of the normal development of the lower genital tract in the female fetus (3). It is one of the congenital disorders that are assessed to be 6 in each 100,000 female births (1). I describe the first case of persistent urogenital sinus in a grown-up lady with a new level

CASE REPORT

DISCUSSION