A Rare Case of Oeis Complex

Abstract

OEIS complex is a rare and complex anomaly of the genitourinary and intestinal tract. It includes Omphalocele, Exstrophy of cloaca, Imperforate anus and Spinal defects. Cloacal exstrophy is considered the most severe ventral abdominal wall defect. The defect occurs due to failure of convergence of mesodermal migrations and inability of development of urorectal septum during embryonic life. The failure of these two events to occur manifests as exstrophy of bladder and bowel. Diagnosis is primarily based on the presenting features. Management requires initial resuscitation and stabilization followed by either single staged closure or multi-stage procedures by multi-disciplinary surgical team. We are reporting a case of classical case of OEIS complex managed successfully at our center.