A rare case of low-grade appendiceal mucinous neoplasm with serosal involvement: a case report

Abstract

Low-grade appendiceal mucinous neoplasm (LAMN) is a malignant lesion of the appendix with an unknown etiology. It is a rare occurrence and incidental finding with only a few cases documented in literature. We present the case of a 55-year-old male with a 5-day history of diffuse abdominal pain, which then localized to the right lower quadrant (RLQ). Abdominal imaging revealed a soft tissue mass in and around the appendix, eventually leading to the diagnosis of a mucinous tumor. Exploratory laparotomy revealed a mucinous tumor of the appendix with rupture. Appendectomy was performed and the specimen along with the mucinous material was submitted for histology. Histopathological examination confirmed the diagnosis of LAMN with serosal perforation. Postoperatively the patient is stable and doing well on follow up. The patient was referred to oncology for further management. Although, LAMN is rare, there is a lack of standardization of treatment, with the need for development to prevent the latter complication of the ill-fated outcome, pseudomyxoma peritonei (PMP).